{"cited_by_count":301062,"description":"This cluster of papers focuses on the clinicopathologic characteristics, genetic mutations, and treatment strategies for fibrous tumors such as Solitary Fibrous Tumors and Desmoid Tumors. It discusses the identification of recurrent gene fusions, the distinction from histologic mimics, risk assessment models, and the efficacy of various treatments including surgery, radiation therapy, and targeted therapies.","display_name":"Soft tissue tumor case studies","domain_id":"4","external_ids":{"openalex":"https://openalex.org/T11991","wikipedia":"https://en.wikipedia.org/wiki/Fibrous_tumor"},"field_id":"27","id":"T11991","keywords":[{"display_name":"aggressive fibromatosis","id":"desmoid-tumor","score":0.7272,"url":"https://openalex.org/keywords/desmoid-tumor"},{"display_name":"solitary fibrous tumor","id":"solitary-fibrous-tumor","score":0.795,"url":"https://openalex.org/keywords/solitary-fibrous-tumor"},{"display_name":"dermatofibrosarcoma protuberans","id":"dermatofibrosarcoma-protuberans","score":0.6861,"url":"https://openalex.org/keywords/dermatofibrosarcoma-protuberans"},{"display_name":"hemangiopericytoma","id":"hemangiopericytoma","score":0.5036,"url":"https://openalex.org/keywords/hemangiopericytoma"},{"display_name":"spindle cell tumor","id":"spindle-cell-tumor","score":0.2211,"url":"https://openalex.org/keywords/spindle-cell-tumor"},{"display_name":"dermatofibroma","id":"dermatofibroma","score":0.3821,"url":"https://openalex.org/keywords/dermatofibroma"},{"display_name":"nodular fasciitis","id":"nodular-fasciitis","score":0.5893,"url":"https://openalex.org/keywords/nodular-fasciitis"},{"display_name":"pediatric soft tissue tumor","id":"pediatric-soft-tissue-tumor","score":0.3215,"url":"https://openalex.org/keywords/pediatric-soft-tissue-tumor"},{"display_name":"pleural neoplasms","id":"pleural-tumors","score":0.2587,"url":"https://openalex.org/keywords/pleural-tumors"},{"display_name":"fibromatosis","id":"fibromatosis","score":0.4404,"url":"https://openalex.org/keywords/fibromatosis"},{"display_name":"benign soft tissue tumor","id":"benign-soft-tissue-tumor","score":0.2031,"url":"https://openalex.org/keywords/benign-soft-tissue-tumor"},{"display_name":"abdominal wall tumor","id":"abdominal-wall-tumor","score":0.3562,"url":"https://openalex.org/keywords/abdominal-wall-tumor"},{"display_name":"malignant solitary fibrous tumor","id":"malignant-solitary-fibrous-tumor","score":0.9095,"url":"https://openalex.org/keywords/malignant-solitary-fibrous-tumor"},{"display_name":"solitary fibrous tumor of the pleura","id":"solitary-fibrous-tumor-of-the-pleura","score":0.8714,"url":"https://openalex.org/keywords/solitary-fibrous-tumor-of-the-pleura"},{"display_name":"infantile myofibromatosis","id":"infantile-myofibromatosis","score":0.8239,"url":"https://openalex.org/keywords/infantile-myofibromatosis"},{"display_name":"desmoid fibromatosis","id":"desmoid-fibromatosis","score":0.7463,"url":"https://openalex.org/keywords/desmoid-fibromatosis"},{"display_name":"mesenteric tumor","id":"mesenteric-tumor","score":0.2185,"url":"https://openalex.org/keywords/mesenteric-tumor"},{"display_name":"mesenteric fibromatosis","id":"mesenteric-fibromatosis","score":0.8638,"url":"https://openalex.org/keywords/mesenteric-fibromatosis"},{"display_name":"elastofibroma dorsi","id":"elastofibroma-dorsi","score":0.4975,"url":"https://openalex.org/keywords/elastofibroma-dorsi"},{"display_name":"NAB2-STAT6 fusion","id":"nab2-stat6-fusion","score":0.8573,"url":"https://openalex.org/keywords/nab2-stat6-fusion"},{"display_name":"CD34 immunohistochemistry","id":"cd34-immunohistochemistry","score":0.4495,"url":"https://openalex.org/keywords/cd34-immunohistochemistry"},{"display_name":"benign fibrous tumor","id":"benign-fibrous-tumor","score":0.6123,"url":"https://openalex.org/keywords/benign-fibrous-tumor"},{"display_name":"extrapleural solitary fibrous tumor","id":"extrapleural-solitary-fibrous-tumor","score":0.9745,"url":"https://openalex.org/keywords/extrapleural-solitary-fibrous-tumor"},{"display_name":"extra-abdominal desmoid","id":"extra-abdominal-desmoid","score":0.9112,"url":"https://openalex.org/keywords/extra-abdominal-desmoid"},{"display_name":"myofibroma","id":"myofibroma","score":0.4937,"url":"https://openalex.org/keywords/myofibroma"}],"legacy_keywords":["Solitary Fibrous Tumor","Desmoid Tumor","NAB2-STAT6 gene fusions","Surgery","Radiation Therapy","CTNNB1 mutations","Aggressive Fibromatosis","Imatinib treatment","PDGFRB mutations","Prognostic Factors"],"openalex_id":"https://openalex.org/T11991","source_created_date":"2024-01-23T15:27:12","source_updated_date":"2026-10-17T03:02:00","subfield_id":"2745","url":"/topics/T11991","works_api_url":"https://api.openalex.org/works?filter=topics.id:T11991","works_count":34144,"label":"Soft tissue tumor case studies","provider":"openalex","revision":"9d3681794ac46a78","taxonomy_revision":"f050b5d4780b1289","title":"Soft tissue tumor case studies","kind":"topic-directory","aeo_cohort":"topic-directory","catalogue_revision":"f050b5d4780b1289","numeric_address":"36249527338822062","address_version":"morton4x16-v1","coordinates":[4,27,2745,11991],"answer_status":"Directory metadata; local answer requires separate source review","truth_status":"Subject descriptor, not a factual answer or a demonstrated knowledge gap","reviewed_answer":null}