{"cited_by_count":396281,"description":"This cluster of papers focuses on the pathogenesis, diagnosis, and treatment of pemphigoid diseases, particularly bullous pemphigoid and pemphigus vulgaris. It covers topics such as autoantibodies, rituximab therapy, epidemiology, and the use of immunosuppressive therapy including intravenous immunoglobulin. The research also delves into the role of desmoglein in disease pathology and autoimmune mechanisms.","display_name":"Autoimmune Bullous Skin Diseases","domain_id":"4","external_ids":{"openalex":"https://openalex.org/T11730","wikipedia":"https://en.wikipedia.org/wiki/Bullous_pemphigoid"},"field_id":"27","id":"T11730","keywords":[{"display_name":"autoimmune blistering disease","id":"autoimmune-blistering-disease","score":0.9045,"url":"https://openalex.org/keywords/autoimmune-blistering-disease"},{"display_name":"bullous pemphigoid","id":"bullous-pemphigoid","score":0.8508,"url":"https://openalex.org/keywords/bullous-pemphigoid"},{"display_name":"pemphigus vulgaris","id":"pemphigus-vulgaris","score":0.8391,"url":"https://openalex.org/keywords/pemphigus-vulgaris"},{"display_name":"pemphigus","id":"pemphigus","score":0.8073,"url":"https://openalex.org/keywords/pemphigus"},{"display_name":"pemphigus foliaceus","id":"pemphigus-foliaceus","score":0.8884,"url":"https://openalex.org/keywords/pemphigus-foliaceus"},{"display_name":"blistering skin disease","id":"blistering-skin-disease","score":0.4276,"url":"https://openalex.org/keywords/blistering-skin-disease"},{"display_name":"direct immunofluorescence","id":"direct-immunofluorescence","score":0.3837,"url":"https://openalex.org/keywords/direct-immunofluorescence"},{"display_name":"mucous membrane pemphigoid","id":"mucous-membrane-pemphigoid","score":0.8182,"url":"https://openalex.org/keywords/mucous-membrane-pemphigoid"},{"display_name":"basement membrane zone","id":"dermal-epidermal-junction","score":0.2922,"url":"https://openalex.org/keywords/dermal-epidermal-junction"},{"display_name":"epidermolysis bullosa acquisita","id":"epidermolysis-bullosa-acquisita","score":0.4832,"url":"https://openalex.org/keywords/epidermolysis-bullosa-acquisita"},{"display_name":"bullous pemphigus","id":"bullous-pemphigus","score":0.731,"url":"https://openalex.org/keywords/bullous-pemphigus"},{"display_name":"acantholysis","id":"acantholysis","score":0.5198,"url":"https://openalex.org/keywords/acantholysis"},{"display_name":"linear IgA bullous dermatosis","id":"linear-iga-dermatosis","score":0.7974,"url":"https://openalex.org/keywords/linear-iga-dermatosis"},{"display_name":"desmoglein 3","id":"desmoglein-3","score":0.7159,"url":"https://openalex.org/keywords/desmoglein-3"},{"display_name":"paraneoplastic pemphigus","id":"paraneoplastic-pemphigus","score":0.7972,"url":"https://openalex.org/keywords/paraneoplastic-pemphigus"},{"display_name":"dermatitis herpetiformis","id":"dermatitis-herpetiformis","score":0.3155,"url":"https://openalex.org/keywords/dermatitis-herpetiformis"},{"display_name":"desmoglein 1","id":"desmoglein-1","score":0.5701,"url":"https://openalex.org/keywords/desmoglein-1"},{"display_name":"BP180","id":"bp180","score":0.8368,"url":"https://openalex.org/keywords/bp180"},{"display_name":"pemphigoid","id":"pemphigoid","score":0.7265,"url":"https://openalex.org/keywords/pemphigoid"},{"display_name":"drug-induced pemphigus","id":"drug-induced-pemphigus","score":0.8936,"url":"https://openalex.org/keywords/drug-induced-pemphigus"},{"display_name":"subepidermal blistering","id":"subepidermal-blistering","score":0.7398,"url":"https://openalex.org/keywords/subepidermal-blistering"},{"display_name":"mucosal involvement","id":"mucosal-involvement","score":0.2656,"url":"https://openalex.org/keywords/mucosal-involvement"},{"display_name":"pemphigoid gestationis","id":"pemphigoid-gestationis","score":0.8336,"url":"https://openalex.org/keywords/pemphigoid-gestationis"},{"display_name":"BP230","id":"bp230","score":0.8607,"url":"https://openalex.org/keywords/bp230"},{"display_name":"pemphigus vegetans","id":"pemphigus-vegetans","score":0.8993,"url":"https://openalex.org/keywords/pemphigus-vegetans"}],"legacy_keywords":["Pemphigoid","Autoantibodies","Rituximab","Bullous Pemphigoid","Desmoglein","Autoimmune","Immunosuppressive Therapy","Diagnosis","Epidemiology","Intravenous Immunoglobulin"],"openalex_id":"https://openalex.org/T11730","source_created_date":"2024-01-23T15:27:11","source_updated_date":"2026-10-17T03:02:00","subfield_id":"2734","url":"/topics/T11730","works_api_url":"https://api.openalex.org/works?filter=topics.id:T11730","works_count":34387,"label":"Autoimmune Bullous Skin Diseases","provider":"openalex","revision":"94edf62c5d0d5522","taxonomy_revision":"f050b5d4780b1289","title":"Autoimmune Bullous Skin Diseases","kind":"topic-directory","aeo_cohort":"topic-directory","catalogue_revision":"f050b5d4780b1289","numeric_address":"36249011942483426","address_version":"morton4x16-v1","coordinates":[4,27,2734,11730],"answer_status":"Directory metadata; local answer requires separate source review","truth_status":"Subject descriptor, not a factual answer or a demonstrated knowledge gap","reviewed_answer":null}